Hypercapnia enhances airway smooth muscle contractility via STIM1-dependent Ca2+ signaling

Hypercapnia, elevated carbon dioxide (CO2), is common in advanced chronic obstructive pulmonary disease (COPD) and predicts poor clinical outcomes. Traditionally considered a consequence of disease severity, hypercapnia may drive disease progression by promoting airway dysfunction. Here, we show that hypercapnia acts as an active stressor, driving airway smooth muscle (ASM) constriction through a stromal interaction molecule 1-dependent (STIM1-dependent) pathway. Hypercapnia rapidly activates ERK, triggering sarcoplasmic reticulum calcium (Ca2+) release via phosphorylation of the inositol 1,4,5-trisphosphate receptor. ERK also induces nuclear translocation of the transcription factor c-Fos, enhancing STIM1 transcription. These responses were observed under both supraphysiological (~120 mmHg) and clinically relevant (50-60 mmHg) hypercapnia. Increased STIM1 abundance sustains store-operated Ca2+ entry (SOCE), amplifying ASM signaling. In mice, hypercapnia increased ASM and airway contractility in a STIM1-dependent manner. Human genetic analyses revealed noncoding STIM1 variants associated with reduced lung expression that were enriched in patients with COPD. These variants correlated with lower airway resistance under normocapnia; however, this benefit was lost during hypercapnia, indicating a potential gene-environment interaction. Together, our findings position STIM1 as a key mechanistic node linking hypercapnia to Ca2+ dysregulation and airway obstruction, defining a CO2/ERK/STIM1/SOCE axis with translational relevance to chronic lung disease.

  • Shigemura, M.
  • Kryvenko, V.
  • Pacheco, J. A.
  • Puckelwartz, M. J.
  • Aleksic, M.
  • Magnani, N. D.
  • Thompson, E.
  • Martin-Romero, F. J.
  • Cummins, E. P.
  • Seeger, W.
  • Brauninger, A.
  • Welch, L. C.
  • Budinger, G. R. S.
  • Lecuona, E.
  • Dada, L. A.
  • Bharat, A.
  • Vadasz, I.
  • Prakriya, M.
  • Sznajder, J. I.

Keywords

  • *Stromal Interaction Molecule 1/metabolism/genetics
  • Animals
  • Mice
  • Humans
  • *Hypercapnia/metabolism/physiopathology
  • *Calcium Signaling
  • *Muscle, Smooth/metabolism/physiopathology
  • *Muscle Contraction/physiology
  • *Pulmonary Disease, Chronic Obstructive/metabolism/physiopathology
  • Male
  • Calcium/metabolism
  • Sarcoplasmic Reticulum/metabolism
  • Female
  • *Neoplasm Proteins/metabolism/genetics
  • Lung/metabolism
  • Copd
  • Calcium signaling
  • Cell biology
  • Cell stress
  • Muscle biology
  • Pulmonology
Publication details
DOI: 10.1172/jci.insight.202475
Journal: JCI Insight
Number: 17
Work Type: Original
Access number: 42461694
See publication on PubMed
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